Treatment for Cystic Fibrosis
Your child's health care provider will figure out the best treatment for your child
How old your child is
His or her overall health and medical history
How sick your child is
Your child's tolerance for specific medications, procedures, or therapies
Your opinion or preference
There is no cure for CF. However, research in gene therapy is being done. The gene
that causes CF has been found. This may lead to an increased understanding of the
disease. Gene therapy research may eventually cure, prevent, or slow progression of
the disease. Goals of treatment are to ease severity of symptoms and slow the progress
of the disease. Treatment may include:
Management of problems that cause lung obstruction, such as:
Chest physical therapy. This helps loosen and clear lung secretions. Treatment may include postural drainage,
and devices, such as a percussor or flutter, which vibrate the chest wall and loosen
secretions. Chest physical therapy can be done manually or mechanically, with a vest.
Exercise. This helps loosen mucus, stimulate coughing, and improve overall physical condition.
Medications, such as bronchodilators and anti-inflammatories. These are used to decrease inflammation and swelling, thin the mucus, open airways, and
Antibiotics. These are used to treat infections.
Management of digestive problems, which may involve:
Changing your child's diet
Pancreatic enzymes to aid digestion
Treatments for intestinal obstructions
Psychosocial support. Provides help in dealing with coping, independence, sterility,
and sexuality, financial issues, and relationships.
As lung disease gets near the end stage, lung transplantation may be an option. The
type of transplant done is usually a double lung transplant, because leaving the other,
sicker lung in place puts it at risk for infection and damage. Not everyone is a candidate
for a lung transplant. Ask your child's health care provider for more information.
With medical and psychosocial support, many children and adolescents with CF can cope
well and lead a productive life.