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George A. Porter, M.D., Ph.D.

Pediatrics

Publications

Showing all 23 journal articles & 0 books available

Journal Articles

2/2017
Mnatsakanyan N, Beutner G, Porter GA, Alavian KN, Jonas EA. "Physiological roles of the mitochondrial permeability transition pore." Journal of bioenergetics and biomembranes.. 2017 Feb 0; 49(1):13-25. Epub 2016 Feb 11.

9/3/2016
Beutner G, Kambiz AN, Jonas EA, Porter GA. "The Mitochondrial Permeability Transition Pore and ATP Synthase." Handbook of experimental pharmacology.. 2016 Sep 3; Epub 2016 Sep 03.

2/17/2016
Maruyama EO, Lin H, Chiu SY, Yu HM, Porter GA, Hsu W. "Extraembryonic but not embryonic SUMO-specific protease 2 is required for heart development." Scientific reports.. 2016 Feb 17; 6:20999. Epub 2016 Feb 17.

12/4/2015
Homsy J, Zaidi S, Shen Y, Ware JS, Samocha KE, Karczewski KJ, DePalma SR, McKean D, Wakimoto H, Gorham J, Jin SC, Deanfield J, Giardini A, Porter GA, Kim R, Bilguvar K, López-Giráldez F, Tikhonova I, Mane S, Romano-Adesman A, Qi H, Vardarajan B, Ma L, Daly M, Roberts AE, Russell MW, Mital S, Newburger JW, Gaynor JW, Breitbart RE, Iossifov I, Ronemus M, Sanders SJ, Kaltman JR, Seidman JG, Brueckner M, Gelb BD, Goldmuntz E, Lifton RP, Seidman CE, Chung WK. "De novo mutations in congenital heart disease with neurodevelopmental and other congenital anomalies." Science.. 2015 Dec 4; 350(6265):1262-6.

9/2015
Jonas EA, Porter GA, Beutner G, Mnatsakanyan N, Alavian KN. "Cell death disguised: The mitochondrial permeability transition pore as the c-subunit of the F(1)F(O) ATP synthase." Pharmacological research.. 2015 Sep 0; 99:382-92. Epub 2015 May 05.

7/22/2014
Alavian KN, Beutner G, Lazrove E, Sacchetti S, Park HA, Licznerski P, Li H, Nabili P, Hockensmith K, Graham M, Porter GA, Jonas EA. "An uncoupling channel within the c-subunit ring of the F1FO ATP synthase is the mitochondrial permeability transition pore." Proceedings of the National Academy of Sciences of the United States of America.. 2014 Jul 22; 111(29):10580-5. Epub 2014 Jun 16.

6/15/2014
Porter GA, Urciuoli WR, Brookes PS, Nadtochiy SM. "SIRT3 deficiency exacerbates ischemia-reperfusion injury: implication for aged hearts." American journal of physiology. Heart and circulatory physiology.. 2014 Jun 15; 306(12):H1602-9. Epub 2014 Apr 18.

2014
Jonas EA, Porter GA, Alavian KN. "Bcl-xL in neuroprotection and plasticity." Frontiers in physiology. 2014 5:355. Epub 2014 Sep 17.

2014
Beutner G, Eliseev RA, Porter GA. "Initiation of electron transport chain activity in the embryonic heart coincides with the activation of mitochondrial complex 1 and the formation of supercomplexes." PloS one. 2014 9(11):e113330. Epub 2014 Nov 26.

6/13/2013
Zaidi S, Choi M, Wakimoto H, Ma L, Jiang J, Overton JD, Romano-Adesman A, Bjornson RD, Breitbart RE, Brown KK, Carriero NJ, Cheung YH, Deanfield J, DePalma S, Fakhro KA, Glessner J, Hakonarson H, Italia MJ, Kaltman JR, Kaski J, Kim R, Kline JK, Lee T, Leipzig J, Lopez A, Mane SM, Mitchell LE, Newburger JW, Parfenov M, Pe'er I, Porter G, Roberts AE, Sachidanandam R, Sanders SJ, Seiden HS, State MW, Subramanian S, Tikhonova IR, Wang W, Warburton D, White PS, Williams IA, Zhao H, Seidman JG, Brueckner M, Chung WK, Gelb BD, Goldmuntz E, Seidman CE, Lifton RP. "De novo mutations in histone-modifying genes in congenital heart disease." Nature.. 2013 Jun 13; 498(7453):220-3. Epub 2013 May 12.

2/15/2013
, Gelb B, Brueckner M, Chung W, Goldmuntz E, Kaltman J, Kaski JP, Kim R, Kline J, Mercer-Rosa L, Porter G, Roberts A, Rosenberg E, Seiden H, Seidman C, Sleeper L, Tennstedt S, Kaltman J, Schramm C, Burns K, Pearson G, Rosenberg E. "The Congenital Heart Disease Genetic Network Study: rationale, design, and early results." Circulation research.. 2013 Feb 15; 112(4):698-706.

10/12/2012
Walters AM, Porter GA, Brookes PS. "Mitochondria as a drug target in ischemic heart disease and cardiomyopathy." Circulation research.. 2012 Oct 12; 111(9):1222-36.

9/13/2011
Hom JR, Quintanilla RA, Hoffman DL, de Mesy Bentley KL, Molkentin JD, Sheu SS, Porter GA. "The permeability transition pore controls cardiac mitochondrial maturation and myocyte differentiation." Developmental cell.. 2011 Sep 13; 21(3):469-78.

5/2011
Porter GA, Hom J, Hoffman D, Quintanilla R, de Mesy Bentley K, Sheu SS. "Bioenergetics, mitochondria, and cardiac myocyte differentiation." Progress in pediatric cardiology.. 2011 May 0; 31(2):75-81.

2010
Hom J, Yu T, Yoon Y, Porter G, Sheu SS. "Regulation of mitochondrial fission by intracellular Ca2+ in rat ventricular myocytes." Biochimica et biophysica acta.. 2010 1797(6-7):913-21. Epub 2010 Mar 27.

2/10/2006
Lakhani SA, Masud A, Kuida K, Porter GA, Booth CJ, Mehal WZ, Inayat I, Flavell RA. "Caspases 3 and 7: key mediators of mitochondrial events of apoptosis." Science.. 2006 Feb 10; 311(5762):847-51.

6/2003
Porter GA, Makuck RF, Rivkees SA. "Intracellular calcium plays an essential role in cardiac development." Developmental dynamics : an official publication of the American Association of Anatomists.. 2003 Jun 0; 227(2):280-90.

8/9/2002
Porter GA, Makuck RF, Rivkees SA. "Reduction in intracellular calcium levels inhibits myoblast differentiation." The Journal of biological chemistry.. 2002 Aug 9; 277(32):28942-7. Epub 2002 May 31.

8/6/2002
Rentschler S, Zander J, Meyers K, France D, Levine R, Porter G, Rivkees SA, Morley GE, Fishman GI. "Neuregulin-1 promotes formation of the murine cardiac conduction system." Proceedings of the National Academy of Sciences of the United States of America.. 2002 Aug 6; 99(16):10464-9. Epub 2002 Jul 29.

8/2001
Porter GA, Rivkees SA. "Ontogeny of humoral heart rate regulation in the embryonic mouse." American journal of physiology. Regulatory, integrative and comparative physiology.. 2001 Aug 0; 281(2):R401-7.

1997
Porter GA, Scher MG, Resneck WG, Porter NC, Fowler VM, Bloch RJ. "Two populations of beta-spectrin in rat skeletal muscle." Cell motility and the cytoskeleton. 1997 37(1):7-19.

6/1992
Porter GA, Dmytrenko GM, Winkelmann JC, Bloch RJ. "Dystrophin colocalizes with beta-spectrin in distinct subsarcolemmal domains in mammalian skeletal muscle." The Journal of cell biology.. 1992 Jun 0; 117(5):997-1005.

1987
Murphy, CK.; Porter, GA.; Klebba, PE. "Heat modifiability of the Escherichia coli iron-regulated membrane proteins." Membrane Proteins, Proceedings of the Membrane Protein Symposium. 1987; : 149-160.